A Case of Endodermal Sinus Tumor of the Orbit.

Oh, Myung Ju; Lee, Kyung Moo; Min, Byung Moo

Case Report

Journal of the Korean Ophthalmological Society 1989;30(1):137-141.
Published online January 1, 1989.

A Case of Endodermal Sinus Tumor of the Orbit.

Myung Ju Oh, Kyung Moo Lee, Byung Moo Min

Department of Ophthalmology, Chungnam National University, College of Medicine, Korea.

안와에 발생한 Endodermal Sinus Tumor 1 예

오명주(Myung Ju Oh),이경무(Kyung Moo Lee),민병무(Byung Moo Min)

Abstract

A 3-year-old girl with rapidly progressive proptosis had an unusual malignant germ cell tumor of the orbit identified as an endodermal sinus tumor. The endodermal sinus tumor is a malignant germ cell neoplasm that usually arises in gonads, but on rare ocassion ocurrs in extragonadal locations. Histologic examination revealed pseudo papillary pattern that on occasion created peculiar organoid structure similar to the glomeruli(Shiller-Dubal bodies). The patient was treated with exenteration of left orbit and three drug chemotherapy. The present case is of particular interest because of the rarity of extragonadal endodermal sinus tumor.

Key Words: endodermal sinus tumor;germ cell tumor;Schiller-Oubal bodies;exenteration;chemotherapy