Congenital Herditary Stromal Dystrophy of the Cornea.

Ryu, Si Il; Kim, Hyung Jun; Kwak, Jyung Sik

Original Article

Journal of the Korean Ophthalmological Society 1991;32(1):1-8.
Published online January 1, 1991.

Congenital Herditary Stromal Dystrophy of the Cornea.

Si Il Ryu, Hyung Jun Kim, Jyung Sik Kwak

¹Department of Ophthalmology, Daegu Catholic Hospital, Korea.
²Department of Pathology, KyungPook National University School of Medicine, Korea.

선천성 유전성 각막 실질변성

류시일(Si Il Ryu),김형준(Hyung Jun Kim),곽정식(Jyung Sik Kwak)

Abstract

In 1978, a nonprogressive corneal dystrophy was seperated from other causes of congenital opacification on the basis of unique clinincal findings and characteristic electronmicroscopic findings. This disorder, termed congenital hereditary stromal dystrophy, appears to the result of disordered stromal fibrogenesis. Recently, the autors have experienced 4 members of a family with typical electronmicroscopic findings of congenital heaeditary stromal dystrophy of the cornea. In this report we describe the characteristic findings of congenital hereditary stromal dystrophy.

Key Words: congenital hereditary stromal dystrophy;stromal fibrogenesis