Congenital Ocular Motor Apraxia.

Kim, Woo Jung; Chang, Bong Leen

Original Article

Journal of the Korean Ophthalmological Society 1992;33(3):263-267.
Published online March 1, 1992.

Congenital Ocular Motor Apraxia.

Woo Jung Kim, Bong Leen Chang

Department of Ophthalmology, Collge of Medicine, Seoul National University, Seoul, Korea.

편측에 발생한 선천성 안구 운동 실행증 1 예

김우중(Woo Jung Kim),장봉린(Bong Leen Chang)

Abstract

Congenital ocular motor apraxia (COA), first described by Cogan in 1953, is a rare disorder which shows characteristic defect of horizontal voluntary saccades and head thrust. Until now, most cases have showed presumably congenital in origin, bilaterality, and tendency of various recovery with aging. But the causes and mechanisms of COA are not known. Occasionally, it combines with other neurologic abnormalities and the metabolic diseases such as Gaucher's disease which exhibits similar clinical characteristics of COA. We recently experienced a 3 years old girl who showed clinical features of unilateral congenital ocular motor apraxia.

Key Words: Head thrust;Unilateral congenital ocular motor apraxia;Voluntary saccades