A Case of Benign Nonte ratoid Medulloepithelioma of the Optic Nerve Head.

Kim, Jung Hwan; Park, Eon Sup; Yang, Han Nam

Case Report

Journal of the Korean Ophthalmological Society 1999;40(6):1727-1731.
Published online June 1, 1999.

A Case of Benign Nonte ratoid Medulloepithelioma of the Optic Nerve Head.

Jung Hwan Kim, Eon Sup Park, Han Nam Yang

Department of Ophthalmology, College of Medicine, Chung-ang University.

시신경 유두부에 발생한 수질상피종 1예 보고

김정환(Jung Hwan Kim),박언섭(Eon Sup Park),양한남(Han Nam Yang)

Abstract

Medulloepithelioma(diktyoma) is a uncommon congenital tumor that is generally believed to arise from the embryonic neuroepithelium of the medullary tube. This tumor usually arises from the ciliary body epithelium. But medulloepitheliomas of the retina and optic nerve may also occur, although it is extremely rare, because the embryonal medullary epithelium that lines the optic vesicle is continuous with the epithelium lining the cavity of the optic nerve during the early embryonal period. The occurrence of medulloepithelioma of the optic nerve is exceptionally rare, with only a few cases have been previously reported. We report a first case of medulloep-ithelioma of the optic nerve head in Korea in a 5-year-old girl who presented with a poor vision and squint of the left eye.

Key Words: Medulloepithelioma;Optic nerve head