A Case of Bilateral Persistent Hyperplastic Primary Vitreous.

Kim, Jin Kuk; Lee, Jong Bok; Kim, Hong BoK

Case Report

Journal of the Korean Ophthalmological Society 1989;30(2):311-314.
Published online February 1, 1989.

A Case of Bilateral Persistent Hyperplastic Primary Vitreous.

Jin Kuk Kim, Jong Bok Lee, Hong BoK Kim

Department of Ophthalmology, Yonsei University, College of Medicine, Seoul, Korea.

양안에 발생한 증식성 일차 초자체 잔류 1 예

김홍복(Hong Bok Kim),김진국(Jin Kuk Kim),이종복(Jong Bok Lee)

Abstract

Persistent hyperplastic primary vitreous(PHPV) is a congnital abnormality of the embryonic intraocular vasculature, resulting from the failure of regression of the primary vitreous in a full-term infant. PHPV is usually unilateral and characterized by leukocoria, elongated ciliary process, microphthalmia, cataract, rubeosis iridis, shallow anterior chamber, and secondary glaucoma. PHPV finally develops into retinal detachment, intractable glaucoma, and pthisis bulbi. Surgical treatment, involving lensectomy and vitrectomy, is not successful and poor visual result is obtained due to retinal abnormalities. A one-month-old girl was found to have persistent hyperplastic primary vitreous in both eyes, and she expired of unknown etiology at home 2 months after diagnosls.

Key Words: Persistent hyperplastic primary vitreous;primary vitreous;secondary vitreous;hyaloid vascular system