A Case of Anterior Lenticonus in Alport's Syndrome.

Lee, Hee La; Rhee, Mi Ri; Shim, Yoon Bo; Kim, Bong Chul

Case Report

Journal of the Korean Ophthalmological Society 1989;30(2):305-309.
Published online February 1, 1989.

A Case of Anterior Lenticonus in Alport's Syndrome.

Hee La Lee, Mi Ri Rhee, Yoon Bo Shim, Bong Chul Kim

Department of Ophthalmology, School of Medicine, Soon Chun Hyang University, Seoul, Korea.

Alport 증후군과 동반된 전원추수정체 1 예

김봉철(Bong Chul Kim),심윤보(Yoon Bo Shim),이희라(Hee La Lee),이미리(Mi Ri Rhee)

Abstract

Alport's syndrome, first described by Alport in 1927, is a clinical entity which consists of lens abnormalities, hereditary hemorrhagic nephritis and nerve deafness. Anterior lenticonus is a rare structual anomaly of lens in which there is a conicalor spherical protrusion of the anterior lens surface into the anterior chamber as a characteristic finding of Alport's syndrome. The authers experienced a case of Alport's syndrome in a 22-year-old man associated with bilateral anterior and posterior lenticonus, hematuria, proteinuria, renal failur earld nerve deafness(complete form).

Key Words: Alport's syndrome;Anterior lenticonus;Hemorrhagic Nephritis;Deafness