J Korean Ophthalmol Soc > Volume 58(1); 2017 > Article
Journal of the Korean Ophthalmological Society 2017;58(1):79-82.
DOI: https://doi.org/10.3341/jkos.2017.58.1.79    Published online January 15, 2017.
A Case of Extensive Epibulbar Choristoma Associated with Microphthalmos.
Do Yeh Yoon, Jinku Park, Namju Kim, Ho Kyung Choung, Sang In Khwarg
1Department of Ophthalmology, Seoul National University Hospital, Seoul, Korea. khwarg@snu.ac.kr
2Department of Ophthalmology, Seoul National University College of Medicine, Seoul, Korea.
3Department of Ophthalmology, Seoul National University Bundang Hospital, Seongnam, Korea.
4Department of Ophthalmology, Seoul Metropolitan Government-Seoul National University Boramae Medical Center, Seoul, Korea.
소안구증에 동반된 광범위한 안구바깥 분리종 1예
윤도예1⋅박진구1⋅김남주2,3⋅정호경2,4⋅곽상인1,2
서울대학교병원 안과1, 서울대학교 의과대학 안과학교실2, 분당서울대학교병원 안과3, 서울대학교병원운영 서울특별시보라매병원 안과4
Abstract
PURPOSE
Choristomas represent congenital overgrowth of normal tissues in an abnormal location. The simultaneous presence of epibulbar choristoma and microphthalmos has rarely been reported. The authors report a case of extensive epibulbar choristoma associated with microphthalmos. CASE SUMMARY: A 9-day-old boy with the left eyeball absent from birth was referred to our clinic. A large cornea-like structure covered by keratinized membrane was observed inside the eyelid aperture, therefore buphthalmos or corneal staphyloma with microphthalmos was presumed. At the age of 2 months, a large mass of central conjunctival sac protruded through the left eyelid aperture. Manual reduction could not return the tissue to its original site and the mass immediately protruded again. At the age of 9 months, orbital magnetic resonance imaging showed the small presumed ocular tissue behind the large mass of fat signal in the central anterior orbit, therefore, extensive epibulbar choristoma associated with microphthalmos was diagnosed. At 12 months of age, partial excision of the protruding portion of the mass was performed. Based on pathologic examination, the mass was determined to be a choristoma and cosmetically acceptable appearance with prosthesis was maintained for 10 months after the surgery. CONCLUSIONS: Because there is no vision in extensive choristoma associated with microphthalmos, the treatment goal is cosmetic improvement. Conjunctivoplasty following partial mass excision for prosthesis wearing is a good treatment option.
Key Words: Epibulbar choristoma;Microphthalmos


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