| Long-term Results of Vision and Fundus Findings in X-linked Juvenile Retinoschisis. |
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Jong Joo Lee, Jeong Hun Kim, Ho Kyung Choung, Jang Won Heo, Seong Joon Kim, Young Suk Yu |
1Department of Ophthalmology, Seoul National University College of Medicine, Seoul, Korea. ysyu@snu.ac.kr
2Seoul National University Boramae Hospital, Seoul, Korea.
3Seoul Artificial Eye Center, Clinical Research Institute, Seoul National University Hospital, Seoul, Korea. |
| 엑스염색체관련 연소망막층간분리의 시력과 안저 소견 |
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이종주1,김정훈1,정호경2,허장원2,김성준1,3,유영석1,3 |
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Department of Ophthalmology, Seoul National University College of Medicine1, Seoul, Korea Seoul National University Boramae Hospital2, Seoul, Korea, Seoul Artificial Eye Center, Clinical Research Institute, Seoul National University Hospital3, Seoul, Korea |
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Correspondence:
유영석 |
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| Abstract |
PURPOSE
To evaluate long-term changes in visual acuity, fundus findings and complications in X-linked juvenile retinoschisis. METHODS: A retrospective chart review was conducted on 48 patients diagnosed with X-linked juvenile retinoschisis and followed for a minimum of 12 months. RESULTS: Forty-eight males (mean age 5.7 years) were followed for a mean of 6.3 years. The mean visual acuities were 0.14 at the initial and most recent examinations without significant change (p=0.67). Macular abnormalities were seen in all eyes. Macular lesions varied as follows: decreased foveal reflex (12.5%), typical foveal schisis (77.1%), atrophic change (5.2%), and macula-involving peripheral schisis (5.2%). When patients had different macular findings, the mean visual acuities were significantly different among groups (p< or =0.005), except those between the atrophic change group and the macula-involving peripheral schisis group. Peripheral schisis was detected in 66% of patients. The fundus findings were stationary during the follow-up period except in complicated cases with vitreous hemorrhage (15.6%). CONCLUSIONS: X-linked juvenile retinoschisis causes bilateral visual acuity loss, affecting maculae. In uncomplicated cases, changes in visual acuity and fundus findings were not significant during the follow-up period. |
| Key Words:
Fundus findings;Visual acuity;X-linked juvenile retinoschisis |
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