Primary Localized Orbital Amyloidosis.

Lee, Jae Hyeun; Kim, Yoon Duck

Case Report

Journal of the Korean Ophthalmological Society 2001;42(12):1793-1797.
Published online December 1, 2001.

Primary Localized Orbital Amyloidosis.

Department of Ophthalmology, Samsung Medical Center, College of Medicine, Sungkyunkwan University, Seoul, Korea. ydkim@smc.samsung.co.kr

일차성 국소성 안와 아밀로이드증 1 례

이재현(Jae Hyeun Lee),김윤덕(Yoon Duck Kim)

Abstract

PURPOSE
Primary localized orbital amyloidosis is a very rare disease and it may deposit in the local area without any other previous disease. It may also form nodules in the cornea, conjunctiva, and eyelid. It may involve levator aponeurosis and extraocular muscles, and develops the various symptoms such as ptosis, opthalmoplegia and proptosis. We experienced this rare disease and report the case with a review of the literature. METHODS: A 54-year old woman who presented with ptosis, exophthalmos and conjunctival mass was diagnosed to have localized orbital amyloidosis by orbital CT and pathological review of conjunctival mass and orbital lesion. No systemic involvement was noted by systemic work up and we confirmed as primary localized orbital amyloidosis. RESULTS: It is a first case of primary localized orbital amyloidosis in Korea and should be differentiated with other diseases with similar symptoms as above.

Key Words: Conjuntival mass;Exophthalmos;Primary localized orbital amyloidosis;Ptosis