Two Cases of Topless Optic Disc Syndrome.

Kim, Tae Woo; Shin, Ki Chul; Kim, Dong Myung

Case Report

Journal of the Korean Ophthalmological Society 2000;41(10):2291-2295.
Published online October 1, 2000.

Two Cases of Topless Optic Disc Syndrome.

Tae Woo Kim, Ki Chul Shin, Dong Myung Kim

Department of Ophthalmology, Seoul National University College of Medicine, 28 Yeongon-dong, Chongro-ku, Seoul, 110-744, Korea.

Topless Optic Disc Syndrome 2 례

김태우(Tae Woo Kim),신기철(Ki Chul Shin),김동명(Dong Myung Kim)

Abstract

Topless optic disc syndrome is considered as congenital optic nerve hypoplasia.The risk factors of this syndrome are female sex, prematurity and history of maternal diabetes.Normal central visual acuity, thinning of superior peripapillary nerve fiber layer and corresponding inferior visual field defects are the characteristic features of this syndrome.Relative superior entrance of central retinal vessels and superior scleral halo can be found in patients with this syndrome. We experienced two cases of topless optic disc syndrome :one was unilateral and the other, bilateral. They had no history of maternal diabetes. Diffuse superior retinal nerve fiber layer atrophy and inferior visual field defects were observed.Pallor of superior optic neural rim, relative superior entrance of central retinal vessels and superior scleral halo were also observed. It will be necessary to differentiate these findings from glaucomatous optic disc damage and visual field defects.

Key Words: Topless optic disc syndrome;Optic nerve hypoplasia;Glaucomatous optic nerve damage