Management of Ectopia Lentis in Children. |
Young Suk Yu, Jae Yoon Awh, Jin Hak Lee |
Department of Ophthalmology, College of Medicine, Seoul National University, Seoul, Korea. |
소아의 선천 수정체탈구의 치료 |
유영석(Young Suk Yu),오재윤(Jae Yoon Awh),이진악(Jin Hak Lee) |
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Abstract |
To know the causes and visual prognosis of ectopia lentis in children, medical records of 41 patients (82 eyes) were retrospectively analysed.The patients were divided into systemic disease-associated, simple, and familial types according to the causes and directions of lens deviation were compared.Surgical methods, pre-and post-operative corrected vision, and complications were investigated. The mean age at diagnosis was 45/12 years old. The decreased vision (87%) and the presence of family history (7.3%) werethe chief complaints on the first examination. According to the causes, 19patients had Marfan syndrome, 14 simple type, and 8 familial type respectively. The directions of lens deviation in Marfan syndrome were different from in simple and familial types. Surgical management have been per-formed in twenty-six patients (44 eyes) on the average 6years of age, and all but one showed an improvement of postoperative corrected vision. One eye presented a dyscoria as a complication. These results are the first report in Korea about the causes and the visual prognosis of ectopia lentis in children and may give us a reference for further management of these patients. |
Key Words:
Children;Ectopia lentis;Marfan syndrome;Surgical methods;Visual prognosis |
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