Electrophysiologic Finding of Retinitis Pigmentosa Inversus and Differential Diagnosis from Peripapillary Choroidal Dystrophy. |
Kyu Heon Han, Jung Woo Kim |
Deoartment of Oohthalmology, School of Medicine, Hallym University, Seoul, Korea. |
역위성망막색소변성증의 전기생리학적 검사소견 및 유두주위맥락이영양증과의 감별진단 |
한규헌(K H Han),김정우(J W Kim) |
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Abstract |
The authors found 3 cases of retinitis pigmentosa inversus who had characteristics that age of onset is between fifth and sixth decade, retinal lesion was seen around the optic disc and along the retinal vascular arcade, margin is discrete, and peripheral retina is morphologically normal. The authors performed routine ophthalmic examination, fluorescein angiography, electroretinography, electro-oculography. Fluorescein angiogram of retinitis pigmentosa inversus showed diffuse hyperfluoresce due to retinal pigment epithelium atrophy and partical hypofluoreseenee due to choriocapillary atrophy. Characteristic electroretinogram findings were moderate decrease of rod function and mild decrease of cone function. The authors also experienced 1 cases of peripapillary choroidal dystrophy and could differentiate it from retinitis pigmentosa inversus. Peripapillary choroidal dystrophy showed similar that of retinitis pigmentosa inversus in electroretinogram test, but showed diffuse and typical hypofluo rescence due to choriocapillary and retinal pigment epithelium atrophy according to the retinal lesion. |
Key Words:
Electro-oculography;Electroretinography;Fluorescein angiography;Peripapillary choroidal dystrophy;Retinitis pigmentosa inversus |
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