A Case of Unilateral Retinitis Pigmentosa. |
Ke Hahn Kim, Young Hoon Park, Duk Kee Hahn |
Department of Ophthalmology, College of Medicine, Yeungnam University, Taegu, Korea. |
일측성 망막색소변성 1예 |
김계한(Ke Hahn Kim),박영훈(Young Hoon Park),한덕기(Duk Kee Hahn) |
|
|
Abstract |
Retinitis pigmentosa has been recognized as a symmetrical, bilateral, hereditary, tapetoretinal degeneration with night blindness, visual field loss, and abnormal ERG. Unilateral retinitis pigmentosa is a rather rare disease. Pedraglia described first reported a case of suspected unilateral retinitis pigmentosa in 1865. Francois and Verriest proposed the following four criteria of the unilateral retinitis pigmentosa: the presence of functional changes ophthalmoscopically typical primary pigmentary degeneration in the affected eye, the absence of a tapetoretinal dystrophy in the fellow eye with normal ERG over five years and exclusion of the inflammatory cause in the affected eye. We report a case of unilateral retinitis pigmentosa in 29 year-old female who has been followed for over five years. |
Key Words:
Abnormal ERG;Night blindness;Unilateral retinitis pigmentosa |
|