A Case of Orbital Langerhans' cell histiocytosis. |
Jung Chul Shin |
Department of Ophthalmology, College of Medicine, Hanyang University, Seoul, Korea. |
안와에 발생한 Langerhans 세포 조직구증 |
신정철(Jung Chul Shin) |
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Abstract |
Langerhans' cell histiocytosis is a rare childhood disease of unknown etiology that is characterized by abnormal proliferation and infiltration of histiocytic cells in various tissues. The authors experienced a case of Langerhans' cell histiocytosis in 4-year-old man who had swelling of the right upper eyelid. Radiologic examination demonstrates a osteolytic soft tissue mass in the right orbit. The light microscopic and electromicroscopic examinations demonstrates a number of histiocytes containing its cytoplasmic racket-shaped Birbeck granule. Then, we confirmed the Langerhans' cell histiocytosis in the right orbit and the radiotherapy was performed. No recurrence occured more than four years after the initial radiotherapy. |
Key Words:
Birbeck granule;Langerhans' cell histiocytosis |