A Case of Pigmented Paravenous Retino-Choroidal Atrophy and Retinitis Pigmentosa.

Cho, Hee Tae; Kim, Si Yeol; Kim, Sang Ha

Case Report

Journal of the Korean Ophthalmological Society 1991;32(10):903-909.
Published online October 1, 1991.

A Case of Pigmented Paravenous Retino-Choroidal Atrophy and Retinitis Pigmentosa.

Hee Tae Cho, Si Yeol Kim, Sang Ha Kim

Department of Ophthalmology, College of Medicine, Kyung Pook National University, Taegu, Korea.

망막색소변성증과 색소성 방정맥 망맥락막위축 1 예

조희태(Hee Tae Cho),김시열(Si Yeol Kim),김상하(Sang Ha Kim)

Abstract

Pigmented paravenous retinochoroidal atrophy(PPRCA) is an uncommon disease that was first reported in 1937 by T.H.Brown. The diagnosis was based on the distinctive fundus appearance of bone corpuscular pigment accumulation, exclusively along the distribution of the retinal vein. Depending on the degree of severity, there may be peripapillary changes, as well as areas of chrioretinal atrophy adjacent to the perivenular pigmentary changes. Although the fundus abnormalities can be mild or severe, retinal function tests indicated that this is geographic and not a generalized disorder. We experienced a case of PPRCA in the left eye a 40 year-old male, which was associated with retinitis pigmentosa in his right eye.

Key Words: PPRCA (pigmeted paravenous retinochoroidal atrophy);Retinitis pigmentosa;Flourescein angiography;Dark adpatometer;Electroretinogram