A Case of Anterior Lenticonus in Alport's Syndrome. |
Hee La Lee, Mi Ri Rhee, Yoon Bo Shim, Bong Chul Kim |
Department of Ophthalmology, School of Medicine, Soon Chun Hyang University, Seoul, Korea. |
Alport 증후군과 동반된 전원추수정체 1 예 |
김봉철(Bong Chul Kim),심윤보(Yoon Bo Shim),이희라(Hee La Lee),이미리(Mi Ri Rhee) |
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Abstract |
Alport's syndrome, first described by Alport in 1927, is a clinical entity which consists of lens abnormalities, hereditary hemorrhagic nephritis and nerve deafness. Anterior lenticonus is a rare structual anomaly of lens in which there is a conicalor spherical protrusion of the anterior lens surface into the anterior chamber as a characteristic finding of Alport's syndrome. The authers experienced a case of Alport's syndrome in a 22-year-old man associated with bilateral anterior and posterior lenticonus, hematuria, proteinuria, renal failur earld nerve deafness(complete form). |
Key Words:
Alport's syndrome;Anterior lenticonus;Hemorrhagic Nephritis;Deafness |
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