A Case of Congenital Aniridia.

Ahn, Sang Ki; Kang, Jin Soo; Shyn, Kyung Hwan

Case Report

Journal of the Korean Ophthalmological Society 1989;30(5):815-818.
Published online May 1, 1989.

A Case of Congenital Aniridia.

Sang Ki Ahn, Jin Soo Kang, Kyung Hwan Shyn

Department of Ophthalmology, Medical School, Chung Ang University, Korea.

선천성 무홍채증 1 예

안상기(Sang Ki Ahn),강진수(Jin Soo Kang),신경환(Kyung Hwan Shyn)

Abstract

Aniridia, a condition which shows only an extremely rudimentary iris, is a re latively rare congenital anomaly. It is almost bilateral and occurs as an autosomal dominant trait. The authors experienced one patient who had congenital aniridia combined with cataract, ectopia lentis, lens coloboma, corneal opacity and nystagmus in both eye. Intracapsular cataract extraction was performed with satisfactory result. The authors report this case with the review of literatures.

Key Words: Aniridia;Cataract;Ectopia lent is;Lens coloboma