J Korean Ophthalmol Soc > Volume 58(4); 2017 > Article
Journal of the Korean Ophthalmological Society 2017;58(4):482-487.
DOI: https://doi.org/10.3341/jkos.2017.58.4.482    Published online April 15, 2017.
Two Cases of Strabismus Surgery in Myotonic Dystrophy.
Seonjoo Kim, Mi Ra Park
Department of Ophthalmology and Visual Science, Yeouido St. Mary's Hospital, College of Medicine, The Catholic University of Korea, Seoul, Korea. eyedocpark@gmail.com
근이영양증 환자에서의 사시수술 2예
가톨릭대학교 의과대학 여의도성모병원 안과 및 시과학교실
Correspondence:  Mi Ra Park,
Email: eyedocpark@gmail.com
Received: 13 October 2016   • Revised: 16 January 2017   • Accepted: 28 March 2017
We report two cases of strabismus on myotonic dystrophy treated with a surgical procedure. CASE SUMMARY: A 49-year-old female with myotonic dystrophy presented with exotropia above 50 prism diopters and limitation of eye movement at nasal and inferior gaze in both eyes. We performed 9.25 mm lateral rectus recession in her right eye and 8.75 mm lateral rectus recession in her left eye. After surgery, she had 40 prism diopter residual exotropia. A 39-year-old female with myotonic dystrophy type 1 had outward deviation of her left eye. Prism cover-uncover test revealed 40 prism diopter exotropia at near distance and 25 prism diopter exotropia at far distance. We performed 6.0 mm lateral rectus recession and 4.5 mm medial rectus tucking in her left eye. Three months after surgery, the prism cover-uncover test showed 10 prism diopter residual intermittent exotropia at near distance and 6 prism diopter residual exophoria at far distance. CONCLUSIONS: Not only cataract and retinal lesion, but also abnormal ocular movement and strabismus due to weakened extraocular muscles can occur in myotonic dystrophy patients. We recommend examination for functions of extraocular motility to diagnose and to treat for maintaining relatively straight alignment.
Key Words: Myotonic dystrophy;Strabismus surgery

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