Sjögren's Reticular Retinal Dystrophy.

Noh, Hoon; Bae, Kunho; Kang, Se Woong

doi:2019.60.9.887

J Korean Ophthalmol Soc > Volume 60(9); 2019 > Article

Case Report

Journal of the Korean Ophthalmological Society 2019;60(9):887-891.
DOI: https://doi.org/10.3341/jkos.2019.60.9.887 Published online September 15, 2019.

Sjögren's Reticular Retinal Dystrophy.

Hoon Noh, Kunho Bae, Se Woong Kang

Department of Ophthalmology, Samsung Medical Center, Sungkyunkwan University School of Medicine, Seoul, Korea. kangsewoong@gmail.com

쇼그렌 격자 모양 망막이상증

노 훈 · 배건호 · 강세웅

성균관대학교 의과대학 삼성서울병원 안과학교실

Correspondence: Se Woong Kang,
Email: kangsewoong@gmail.com

Received: 27 September 2018 • Revised: 5 January 2019 • Accepted: 16 August 2019

Abstract

PURPOSE
To report a rare case of Sjögren's reticular retinal dystrophy. CASE SUMMARY: A 54-year-old male presented with blurred vision and metamorphopsia in both eyes since a few years prior to his initial visit. There was a bilateral reticular network of yellow deposits throughout the posterior pole on fundus examination, which was hyperautofluorescent in fundus autofluorescence photographs. The pigment alterations were more visible with fluorescein angiography, which showed hypofluorescent lesions with hyperfluorescent borders. Spectral-domain optical coherence tomography showed elevations of the outer retina associated with the presence of subretinal hyperreflective material. Based on the conclusive correlation with clinical features, we diagnosed Sjögren's reticular retinal dystrophy. CONCLUSIONS: Sjögren's reticular retinal dystrophy is characterized by its specific pigment changes at the level of clinical manifestations and the retinal pigment epithelium. In cases of Sjögren's reticular retinal dystrophy, close monitoring is required because it has a lifetime risk of choroidal neovascularization.

Key Words: Macular dystrophy;Pattern dystrophy