A Case of Huge Pilocytic Astrocytoma Causing Eyeball Subluxation.

Kim, Eun Yeong; Jung, Su Kyung; Paik, Ji Sun; Yang, Suk Woo

doi:2014.55.10.1543

J Korean Ophthalmol Soc > Volume 55(10); 2014 > Article

Case Report

Journal of the Korean Ophthalmological Society 2014;55(10):1543-1548.
DOI: https://doi.org/10.3341/jkos.2014.55.10.1543 Published online October 15, 2014.

A Case of Huge Pilocytic Astrocytoma Causing Eyeball Subluxation.

Eun Yeong Kim, Su Kyung Jung, Ji Sun Paik, Suk Woo Yang

Department of Ophthalmology and Visual Science, The Catholic University of Korea College of Medicine, Seoul, Korea. yswoph@hanmail.net

안구아탈구를 유발한 거대 소아 털모양별아교세포종 1예

김은영⋅정수경⋅백지선⋅양석우

Department of Ophthalmology and Visual Science, The Catholic University of Korea College of Medicine, Seoul, Korea

Abstract

PURPOSE
To report a relatively rare case of huge pilocytic astrocytoma of the optic nerve and optic chiasm causing eyeball subluxation. CASE SUMMARY: An eight-year-old male presented with proptosis and visual loss in the left eye for one year. The radiological findings showed a 2.9 x 2.7 x 4.2-cm tumor on the left optic nerve and optic chiasm. For diagnosis and treatment, the patient underwent tumor resection and enucleation. Pathohistological analysis of the tumor specimen revealed pilocytic astrocytoma, which is classified by the World Health Organization as a grade I astrocytic tumor. CONCLUSIONS: Astrocytoma is a tumor of the brain that affects children more often than adults. In general, gross-total resection of pilocytic astrocytoma is expected to be curative due to the non-invasive feature of the tumor. Considering pilocytic astrocytoma as differential diagnosis of orbital tumor in children with symptoms of rapidly progressive proptosis and decreased visual acuity is important because occurrence in the optic nerve and optic chiasm is possible.

Key Words: Optic chiasm;Optic nerve;Pilocytic astrocytoma