Retinal Vascular Changes and Treatment of incontinentia Pigmenti Eyes.

Yu, Young Suk; Park, Kyoung Chan

Original Article

Journal of the Korean Ophthalmological Society 1998;39(8):1823-1830.
Published online August 1, 1998.

Retinal Vascular Changes and Treatment of incontinentia Pigmenti Eyes.

¹Department of Ophthalmology, College of Medicine, Seoul National University.
²Department of Dermatology, College of Medicine, Seoul National University.

색소실조증 눈의 망막 혈관 변화와 치료

유영석(Young Suk Yu),박경찬(Kyoung Chan Park)

Abstract

The retinal vascular changes and the results of treatment were studied in five incontinentia pigmenti patients. All patients were female and had a mean follow-up of 4 1/2 years (7 months~7 1/2 years). Abnormal retinal vascular changes included peripheral avascular retina, retinal and preretinal neovascularization, and dilated, tortuous retinal vessels. Two of them were treated; one received a cryotherapy and the other a laser photocoagulation to the avascular retinal area and showed regression of abnormal vessels. At last follow-up, no eye developed retinal detachment, but traction of the peripheral retina by a vitreous band was visible in three patients. One showed a degenerative macula and an atrophy of the retinal pigment epithelium in the papillomacular bundle area. Our result suggests that incontinentia pigmenti eyes may show retinal vascular changes very similar to that in retinopathy of prematurity, and can be effectively treated by destroying an avascualr retina if indicated.

Key Words: Avascular retina;Cryotherapy;Incontinentia pigmenti;Laser photocoagulation;Neovascularization