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Sjögren’s Reticular Retinal Dystrophy
쇼그렌 격자 모양 망막이상증
JKOS 2019 Sep;60(9):887-91
Published online September 15, 2019;
Copyright © 2019 The Korean Ophthalmological Society.
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Hoon Noh, MD, Kunho Bae, MD, Se Woong Kang, MD, PhD
노 훈 · 배건호 · 강세웅

Department of Ophthalmology, Samsung Medical Center, Sungkyunkwan University School of Medicine, Seoul, Korea
성균관대학교 의과대학 삼성서울병원 안과학교실
Received September 27, 2018; Revised January 5, 2019; Accepted August 16, 2019.
This is an Open Access article distributed under the terms of the Creative Commons Attribution Non-Commercial License ( which permits unrestricted non-commercial use, distribution, and reproduction in any medium, provided the original work is properly cited.
Purpose: To report a rare case of Sjögren’s reticular retinal dystrophy.
Case summary: A 54-year-old male presented with blurred vision and metamorphopsia in both eyes since a few years prior to his initial visit. There was a bilateral reticular network of yellow deposits throughout the posterior pole on fundus examination, which was hyperautofluorescent in fundus autofluorescence photographs. The pigment alterations were more visible with fluorescein angiography, which showed hypofluorescent lesions with hyperfluorescent borders. Spectral-domain optical coherence tomography showed elevations of the outer retina associated with the presence of subretinal hyperreflective material. Based on the conclusive correlation with clinical features, we diagnosed Sjögren’s reticular retinal dystrophy.
Conclusions: Sjögren’s reticular retinal dystrophy is characterized by its specific pigment changes at the level of clinical manifestations and the retinal pigment epithelium. In cases of Sjögren’s reticular retinal dystrophy, close monitoring is required because it has a lifetime risk of choroidal neovascularization.
Keywords : Macular dystrophy, Pattern dystrophy


February 2020, 61 (2)